DOI: https://doi.org/10.22141/2224-0586.5.92.2011.143258

Features of anesthesia in a parturient woman with Werdnig-Hoffmann spinal amyotrophy: a clinical case

O.M. Klygunenko, O.V. Maksimova, A.B. Dudas, V.A. Sedinkin

Abstract


The article describes anesthetic management in a parturient woman suffering from spinal muscular atrophy (Werdnig-Hoffmann disease). The delivery was performed by a cesarean section. Considering the presence of significant extragenital pathology and anatomical changes, the method of anesthesia is chosen: total intravenous anesthesia with auxiliary ventilation in combination with infiltration anesthesia of tissues. In view of the substantial atrophy of the muscular system, muscle relaxants were not used. A male infant was born with a body weight of 2800 g, a length of 49 cm, scored 9/9 by the Apgar. The postpartum period was without complications, the condition of the parturient at discharge was satisfactory.

Keywords


spinal amyotrophy; Werdnig-Hoffmann disease; childbirth; anesthesia

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