Aortic dissection as one of the leading causes of death in Marfan syndrome: a clinical case

O.Yu. Shmidt, K.Yu. Prylutska, A.O. Gritsay


Marfan syndrome, along with other hereditary connective tissue diseases, is the second most common cause of aortic aneurysm. The prognosis of patients with aortic aneurysm depends on early diagnosis and, consequently, early surgical treatment. This article presents a clinical case of late diagnosed Marfan syndrome that was complicated by aortic dissection and subsequently (on the background of unstable blood pressure) — by rupture of the ascending aorta.


Marfan syndrome; hereditary connective tissue di­seases; aortic aneurysm; aortic dissection; ruptured aneurysm


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